Long term survival in pediatric hepatic angiosarcoma (PHAS): A case report and review of the literature

• PHAS may be treated successfully with complete gross resection and chemotherapy.
• Chemotherapy regimens for PHAS are not yet standardized.
• Overall results for treatment of PHAS remain poor.

Pediatric hepatic angiosarcoma (PHAS) is extremely rare, with only five reported tumor-free survivors. Aggressive surgical resection and chemotherapy have been the management in all documented survivors of this disease, however no specific treatment guidelines are established. We present a case of PHAS with the longest reported tumor-free survival at over six years off therapy.