tetrahydrobiopterin

در این صفحه تعداد 419 مقاله تخصصی درباره که در نشریه های معتبر علمی و پایگاه ساینس دایرکت (Science Direct) منتشر شده، نمایش داده شده است. برخی از این مقالات، پیش تر به زبان فارسی ترجمه شده اند که با مراجعه به هر یک از آنها، می توانید متن کامل مقاله انگلیسی همراه با ترجمه فارسی آن را دریافت فرمایید.
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Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: HPA; hyperphenylalaninemia; PAH; phenylalanine hydroxylase; BH4; tetrahydrobiopterin; NGS; next generation sequencing; MLPA; multiplex ligation-dependent probe amplification; qRT-PCR; quantitative real-time PCR; APV; allelic phenotype values; GPV; genotyp
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: PKU mouse model; Phenylalanine ammonia lyase; Erythrocytes as drug delivery system; Enzyme replacement therapy; Cognition and PKU; Behavior and PKU; PKU; phenylketonuria; PAH; phenylalanine hydroxylase; Phe; l-phenylalanine; Tyr; l-tyrosine; BH4; tetrahyd
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: Ach; acetylcholine; ARE; antioxidant response element; BH4; Tetrahydrobiopterin; DMNQ; 2,3-Dimethoxy-1,4-naphthoquinone; EDRF; Endothelium-derived relaxing factor; eNOS; Endothelial nitric-oxide synthase; GAPDH; glyceraldehyde 3-phosphate dehydrogenase; G
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: NO; nitric oxide; SNP; sodium nitroprusside; TNG; nitroglycerine; SHR; spontaneously hypertensive rats; TERPY; [Ru(terpy)(bdq)NO]3+; E−; endothelium-denuded; E+; endothelium-intact; 2K; sham-operated rats; 2K-1C; two-kidney one-clip, renal hypertensive
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: AT-MSCs; adipose tissue-derived MSCs; BAT; brown adipose tissue; BH4; tetrahydrobiopterin; BMP; bone morphogenetic protein; DHEA; dehydroepiandrosterone; eWAT; epididymal white adipose tissue; FAs; fatty acids; G3PHD; glycerol 3-phosphate dehydrogenase; H
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: PKU; Phenylketonuria; phe; phenylalanine; %fatmass; percent body fat mass; %FFM; percent fat free mass; P:E ratio; protein to energy ratio; BH4; tetrahydrobiopterin; AAF; amino acid formula; E%BMR; energy intake as a percentage of basal metabolic rate; BI
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: PKU; phenylketonuria; Phe; phenylalanine; PAH; phenylalanine hydroxylase; ACMG; American College of Medical Genetics and Genomics; US; United States; BH4; tetrahydrobiopterin; GMDI; Genetic Metabolic Dietitians International; Phenylketonuria; Adherence; B
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: Algae; Comparative modeling; Evolution; Nitric oxide; Nitric oxide synthase; Nitrate reductase; Nitrite; Land plants; H4B; tetrahydrobiopterin; CaM; calmodulin; NO; nitric oxide; NOS; nitric oxide synthase; NOSoxy; NOS oxygenase domain; NR; nitrate reduct
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: ACh; acetylcholine; ApoB100; apolipoprotein B100; B2M; β2-microglobulin; BH4; tetrahydrobiopterin; CaM; calmodulin; DHE; dihydroxyethidine; E+; ethidium; eNOS; endothelial nitric oxide synthase; EPR; electron paramagnetic resonance; FAD; flavin adenine d
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: ARBs; angiotensin II type 1 receptor blockers; BH4; tetrahydrobiopterin; BMI; body mass index; CABG; coronary artery bypass graft; EPCs; endothelial progenitor cells; ERα; estrogen receptor alpha; ERβ; estrogen receptor beta; GLUT4; glucose transporter
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: ADMA; asymmetric dimethylarginine; AGE; advanced glycation end-products; BH4; tetrahydrobiopterin; CAC; circulating angiogenic cells; CFU/Hill; colony forming unit-Hill; CREB; c-AMP response element-binding protein; CXCR-4; C-X-C chemokine receptor type 4
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: SDF-1; stromal cell-derived factor 1; PAD; peripheral arterial disease; GPx; glutathione peroxidase; TAK1; transforming growth factor-B-activated-kinase 1; PTP1B; protein tyrosine phosphatase 1B; EDRF; endothelial-derived relaxing factor (EDRF); BH4; tetr
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: AGE; advanced-glycation endproducts; BH4; tetrahydrobiopterin; BKCa; large conductance calcium-activated potassium channel; COX; cyclooxygenase; EDH; endothelium-derived hyperpolarisation; eNOS; endothelial nitric oxide synthase; GHB; glycated haemoglobin
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: ADMA; asymmetric dimethylarginine; ALP; alkaline phosphatase; ALT; alanine aminotransferase; AST; aspartate aminotransferase; BH2; dihydrobiopterin; BH4; tetrahydrobiopterin; BW; body weight; CTRL; isocaloric control standard chow diet; DEXA; dual-energy
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: AGEs; advanced glycation end products; LA; alpha lipoic acid; BAEC; bovine aortic endothelial cells; BCA; bicinchoninic acid; BH4; tetrahydrobiopterin; CaI; calcium ionophore; CAT; catalase (EC 1.11.1.6); CMD; cardiometabolic disease; CVD; cardiovascular
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: 5-HIAA; 5-hydroxyindolacetic acid; 5-HT; 5-hydroxytryptamine; 5-HTP; 5- hydroxytryptophan; AADC; aromatic L-amino acid decarboxylase; ADR; acute dystonic reaction; BH4; tetrahydrobiopterin; CSF; cerebrospinal fluid; DRD; dopa-responsive dystonia; dRN; dor
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: BH4; tetrahydrobiopterin; BP; biopterin; i.pl.; intraplantarily; L-NAME; Nω-Nitro-l-arginine methyl ester hydrochloride; L-NNA; Nω-Nitro-L-arginine; NO; nitric oxide; NOS; nitric oxide synthase; PGE2; prostaglandin E2; TRPV; transient receptor potential
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: BH4; tetrahydrobiopterin; DSF; differential scanning fluorimetry; L-Dopa; (S)-3,4-dihydroxyphenylalanine; PAH; phenylalanine hydroxylase; PKU; phenylketonuria; TH; tyrosine hydroxylase; THD; TH deficiency; TPH2; tryptophan hydroxylase isoform 2; PD; Parki
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: 3-NT; 3-nitrotyrosine; ADMA; asymmetric dimethyl arginine; Akt; protein kinase B; AMPK; AMP-activated protein kinase; BAT; brown adipose tissue; BH2; dihydrobiopterin; BH4; tetrahydrobiopterin; BMR; basal metabolic rate; Cav-1; caveolin-1; CCK; cholecysto
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: AAV; adeno-associated virus; ACMG; American College of Medical Genetics and Genomics; AHRQ; Agency for Healthcare Research and Quality; BH4; tetrahydrobiopterin; BMD; bone mineral density; CDE; Common Data Element; CHD; congenital heart disease; CNS; cent
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: DAH7PS; 3-deoxy-D-arabino-heptulosonate 7-phosphate synthase; IEC; ion exchange chromatography; MBP; maltose binding protein; PS; Phenyl Sepharose; Phe; phenylalanine; PAH; phenylalanine hydroxylase; PKU; phenylketonuria; PAGE; polyacrylamide gel electrop
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: A; mitral inflow late filling velocity in pulse-wave Doppler; BDM; 2,3-butanedione monoxime; BH4; tetrahydrobiopterin; DOCA; deoxycorticosterone acetate; E; mitral inflow early filling velocity in pulse-wave Doppler; EF; ejection fraction; FS; fractional
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: AKAP; A-kinase anchor protein; Ang II; angiotensin II; AP; action potential; APD; action potential duration; BH4; tetrahydrobiopterin; cAMP; cyclic adenosine monophosphate; CaM; calmodulin; CaMKII; Ca/calmodulin-dependent protein kinase II; CaMKIIδC; cyt
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: 5-HIAA; 5 hydroxyindoleacetic acid; 5-HT; serotonin; 5-HTT; 5-HT transporter; ACTH; adrenocorticotropic hormone; AIAQ; anger irritability and assault questionnaire; AMPA; α-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid; BCG; bacille Calmette-Gueri
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: BH4; Tetrahydrobiopterin; E. coli; Escherichia coli; ELISA; Enzyme-linked immunosorbent assay; hPAH; Human phenylalanine hydroxylase; IPTG; Isopropyl-β-d-thiogalactoside; kDa; Kilo Dalton; MBP; Maltose binding protein; PAH; Phenylalanine hydroxylase prot
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: Cigarette smoking; Tetrahydrobiopterin; Nitric oxide synthase; Guanosine triphosphate cyclohydrolase; Oxygen free radicals; Ubiquitination; CS; Cigarette smoking; CVD; Cardiovascular disease; ED; Endothelial dysfunction; NO; Nitric oxide; eNOS; Endothelia
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: AADC; aromatic l-amino acid decarboxylase; AR/ADGTPCH; autosomal recessive/dominant GTP-cyclohydrolase deficiency; BH4; tetrahydrobiopterin; DAT; dopamine transporter; DßH; dopamine β-hydroxylase; DHFR; dihydrofolate reductase deficiency; DHPR; dihydrop
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: MPH; maternal physiological hypercholesterolemia; MSPH; maternal supraphysiological hypercholesterolemia; GTP; guanosine triphosphate; GTPCH1; GTP cyclohydrolase 1; DHFR; dihydrofolate reductase; BH2; dihydrobiopterine; BH4; tetrahydrobiopterine; HUVECs;