Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
11010492 | Cor et Vasa | 2018 | 4 Pages |
Abstract
Arrhythmogenic right ventricular dysplasia (ARVD) is a form of inherited cardiomyopathy characterized by fibro-fatty substitution mainly right ventricular (RV). Affected patients may succumb to life-threatening ventricular arrhythmias and heart failure. It is even more common among athletes who experience sudden cardiac death (SCD). The disease involvement is not limited only to the RV, but the left ventricle (LV) can also be involved. We have reported a case of a 38 years-old man, with two episodes of syncope in his history. After echocardiographic investigations, the patient was referred to cardiovascular magnetic resonance (CMR). Morphological images showed fatty infiltration of the epicardial layer of LV lateral wall (mid and apical segment). A diagnosis of 'Isolated Left-Sided Arrhythmogenic Cardiomyopathy' was made. An ICD implantation was performed, and a medical therapy with enalapril and bisoprolol was started.
Keywords
CMRTTEARVDLGESCDImplantable cardioverter defibrillatorVentricular arrhythmiaGadolinium enhancementtransthoracic echocardiogramRight ventricularleft ventricleICDArrhythmogenic right ventricular dysplasiaArrhythmogenic right ventricular dysplasia/cardiomyopathycardiovascular magnetic resonanceSyncopeSudden cardiac deathCardiomyopathy
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Authors
Michele Scarano, Germana Gizzi, Cesare Mantini,