Isolated subglottic stenosis by Wegner's granulomatosis in a pediatric patient – A case report

Wegener's granulomatosis (WG) is a systemic autoimmune lesion of unknown etiology characterized by necrotizing granulomatous inflammation and vasculitis affecting small blood vessels. Although WG is a rare condition in children, it is often confused with more common ailments, so there is delay in confirmation of the diagnosis. We present a 13-year-old boy who came with breathing difficulty. A nasopharyngolaryngoscopy revealed narrowing in the subglottic region. This was managed by planned microlaryngoscopy with cold steel instruments. Excision of granulomatous tissue from subglottis along with application of steroid and mitomycin-C. Biopsy from the subglottic area confirmed the diagnosis of WG. During managing subglottic stenosis (SGS), the etiology of WG should be in mind as it is essential to find out the cause for providing the appropriate treatment. An early diagnosis of WG leads to early initiation of treatment which helps in reduction of morbidity and mortality associated with the disease.