Syndrome d'Ehlers-Danlos et odontologie

Odontologists are more familiar with osteogenesis imperfecta and Marfan's disease, two other inherited diseases of collagen than Ehlers-Danlos syndrome is yet, by far more, common. The oral manifestations are numerous, often disabling functionally. They contribute to the diagnosis and the dentist may be the first practitioner that evokes very rarely diagnosed disease? Shaped anomalies are numerous: the roots are often shorter, it is common to find the enamel hypoplasia. Mucosal fragility is found in three quarters of patients with EDS. The achievement of the temporo-mandibular joints is present in 47% of which may cause postural disorders. The resistance to local anesthetics is usual. There is no risk of oslerian infection even in the presence of cardiac valves modifications. Surgical and orthodontic actions must be atraumatic due to the fragility of all the tissues. An adaptation in each case is required.