Radicular cyst in a patient with untreated Wiskott–Aldrich syndrome: A case report

Wiskott–Aldrich syndrome (WAS) is a condition with variable expression, which causes persistent thrombocytopenia and, in its complete form, also causes small platelets and humoral immunodeficiency. A 14-year-old boy, diagnosed with WAS but never treated, presented with symptoms of heart and renal failure. His right buccal region was swollen and his right first molar showed a cyst-like image on dental X-ray films. The boy's symptoms were attributed to an infected cyst, greatly aggravated by WAS-related immunodeficiency. The boy was sedated and the affected tooth and cyst were enucleated. Invasive treatment was safely achieved by paying close attention to whole-body management.

▸ Wiskott-Aldrich syndrome(WAS) is a congenital X-linked immunodeficiency. ▸ A 14-year-old boy with severe symptoms of cardiac and renal failure. ▸ Large swelling was observed in right buccal region and molar had severe caries. ▸ The affected tooth and cyst were encleated after including deep intravenous sedation. ▸ Platelet transfusions to prevent bleeding and postoperative development of anemia.