Tumor maligno de la vaina del nervio periférico (MPNST) glandular de la órbita: Primera descripción de la literatura de localización orbitaria en un paciente con neurofibromatosis tipo 1

For the first time in the literature a case of Glandular MPNST located at the orbit, which occurred in child with NF1, is described. This extremely uncommon neoplasia must be taken into account, in the study of biphasic malignant lesions, as its diagnosis is of great importance because of the bad prognosis of the affected patients.