L'IRM au centre du diagnostic du syndrome de Susac

Susac's syndrome is a rare clinical triad of encephalopathy, branch retinal artery occlusion (BRAO) and hearing loss. It is a presumably autoimmune endotheliopathy usually affecting young women aged 20-40 years. We report the case of an 18 year-old-woman with meningo-encephalitis of unknown origin. The brain MRI showed hyperintense signals on T2 and microinfarcts involving the thalamus and corpus callosum. The specific imaging abnormalities led to the diagnosis of Susac syndrome. Angiography, used as a secondary investigation technique, and the hearing loss confirmed the diagnosis.