Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
3168175 | Oral Surgery, Oral Medicine, Oral Pathology, Oral Radiology, and Endodontology | 2009 | 7 Pages |
Abstract
The Papillon-Lefevre syndrome (PLS) was first described by Papillon and Lefevre in 1924. It is an autosomal recessive disorder characterized by a diffuse palmoplanter hyperkeratosis and rapidly progressive and devastating periodontitis, affecting the primary as well as the permanent dentition, attributed to a point mutation of the cathepsin C gene. This paper presents a clinical presentation and a brief review of its etiology and treatment modalities.
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Authors
Parmanand J. Dhanrajani,