Juvenile xanthogranuloma: Late presentation of giant form ends with atrophic sequelae: Case report

Juvenile xanthogranuloma (JXG) is a histiocytic disorder that is usually benign and limited to the skin. Usually it regresses spontaneously, more often without or with limited skin changes. The systemic form of JXG is rare and may be associated with severe morbidity and mortality due to CNS involvement. Here, we describe a 15 year old boy with puzzling skin lesions evolving since last 6 months on the neck. A skin biopsy and immunohistochemistry confirmed the diagnosis of JXG.