Restriktive Kardiomyopathie

Restrictive cardiomyopathy is a rare disease, which is characterized by an increased stiffness of the heart with involvement of myocardium, interstitium and endocardium. Many causes are possible. Restrictive cardiomyopathies are classified into primary and secondary forms. The primary forms include idiopathic restrictive cardiomyopathy, Loeffler endocarditis, endomyocardial fibrosis and hypereosinophilic syndrome. Among the secondary forms infiltrative heart diseases like amyloidosis or sarcoidosis and storage diseases like haemochromatosis or glycogen storage diseases can be found. For diagnosis echocardiography, cardiac catheter including invasive pressure measurement and myocardial biopsy, are useful. Treatment is performed according to the primary disease.