Epithelioid angiomyolipoma with involvement of inferior vena cava as a tumor thrombus: A case report

A 27-year-old female with chronic right-side flank pain was diagnosed with renal epithelioid angiomyolipoma (EAML) extending as a thrombus into the renal vein and vena cava. Intravascular extension of EAML is quite rare; however, it may result in fatal complications if not appropriately treated. She successfully underwent a radical nephrectomy and inferior vena caval thrombectomy. Intravascular extension of EAML, although rare, has been reported. We present a new case and a description of the surgical management. Furthermore, we reviewed and analyzed nine case reports of invasive renal EAMLs.

摘要患者，女性，27歲，以右側慢性腰痛為主要症狀，在我院診斷為腎上皮樣血管平滑肌脂肪瘤併發腎靜脈和腔靜脈癌栓。血管侵犯的腎上皮樣血管平滑肌脂肪瘤（EAML）非常罕見，如不正確治療可出现致命併發症。該患者成功接受腎臓根治性切除及下腔靜脈切開癌栓取出術。盡管侵犯血管的腎上皮樣血管平滑肌脂肪瘤（EAML）非常少見，但曾被報導。我們描述了一例新病例及其手術處理方式。此外，我們回顧文獻併分析了至今全球曾報導的9例腎上皮樣血管平滑肌脂肪瘤併發下腔靜脈癌栓的病例。