Disgenesia tubular renal. Una causa infrecuente de oligoamnios

Renal tubular dysgenesis is acquired during fetal development or through autosomal recessive inheritance. Histologically, this entity is a severe disorder affecting renal tubular development. Clinically, renal tubular dysgenesis is characterized by persistent fetal anuria and perinatal demise, probably due to pulmonary hypoplasia and Potter sequence. We report the case of a female neonate who died a few hours after birth from renal and respiratory failure. Post-mortem examination identified renal tubular dysgenesis.