Un fibrome desmoplastique du tibia proximal révélé par une fracture pathologique : un cas rare

Desmoplastic fibroma or desmoid bone tumor is a rare tumor described for the first time by Jaffe in 1958. It accounts 0.3% of all benign bone tumors. Histology is required for certain diagnosis of desmoid fibroma. The tumor is composed of sparse fibroblasts in a rich background of collagen fibers, a histological presentation exactly the same as soft tissue desmoid fibroma. Histological study of this tumor may be difficult. Pathological fracture represents a rare revealing. We report a case of a desmoplastic fibroma of the proximal tibia revelated by a pathological fracture. The observation illustrates differents diagnosis and therapeutic aspects of this tumor. The rate of local recurrence is high in the event of partial resection. Surgery is the optimal treatment, with tumor resection as wide as possible depending on the localization, cimentoplasty and internal fixation.