Article ID Journal Published Year Pages File Type
4112265 International Journal of Pediatric Otorhinolaryngology 2014 4 Pages PDF
Abstract

BackgroundAggressive fibromatosis, previously referred to as desmoid tumor, is a rare tumor. It is classified as benign, however, has a high potential for local invasion and recurrence. It is most commonly found in the abdomen, with an origin in the head and neck accounting for less than a quarter of the total cases.MethodsLiterature review using PubMed and OVID and a combination of the words, “desmoid”, “fibromatosis”, “pediatric”, “children”, and “head and neck”.ResultsAnnual occurrence is 0.2 – 0.4 per 100,000, with origins in the head and neck accounting for 10–25%. Since 1954, 97 cases of pediatric head and neck fibromatosis were reported. The age range was from birth to 16 years, with the average being 4 years and 5 months old. The overwhelming majority of tumors were of the mandible (38%). 74% patients underwent a large resection as the primary treatment modality. The most common treatment complication was tumor recurrence (16%).ConclusionsFibromatosis is a rare tumor of muscoloaponeurotic origin. Surgery is the mainstay of treatment; however recurrence rates are high, even despite negative surgical margins.

Related Topics
Health Sciences Medicine and Dentistry Otorhinolaryngology and Facial Plastic Surgery
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