Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
4112789 | International Journal of Pediatric Otorhinolaryngology | 2012 | 5 Pages |
Abstract
Juvenile dermatomyositis (JDM) is the most common inflammatory autoimmune myopathy in children. Most common presentations consist of heliotrophic rash and/or gottron's papules in addition to proximal muscle weakness. A typical presentations have been reported. We present a 13-year-old African American male who presented with a two-week history of bilateral periorbital edema that was unresponsive to glucocorticoids. He had elevated transaminases but no detectable muscle weakness. A muscle biopsy was consistent with juvenile dermatomyositis. This case highlights the need to consider dermatomyositis in cases of facial swelling and the use of aggressive immunosuppressive therapies due to its associated vasculopathies.
Related Topics
Health Sciences
Medicine and Dentistry
Otorhinolaryngology and Facial Plastic Surgery
Authors
Nishant Dwivedi, Christie Michael, D. Betty Lew, Sandra Arnold, Masanori Igarashi, Tulio Bertorini, Jerome W. Thompson, Linda K. Myers, Monica L. Brown,