Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
4115492 | International Journal of Pediatric Otorhinolaryngology | 2008 | 4 Pages |
Abstract
SummaryNager acrofacial dysostosis is a rare congenital syndrome characterized by malformed mandibulofacial structures and pre-axial upper limbs. Trismus and glossoptosis from mandibular abnormalities predisposes infants to life-threatening respiratory distress. A case of a Nager Syndrome mother delivering a similarly afflicted fetus is presented, with approaches to maintaining both tenuous airways described. Distinguishing this condition from similar syndromes is critical for care and prognosis.
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Authors
Allen S. Ho, Pedram Aleshi, Sheila E. Cohen, Peter J. Koltai, Alan G. Cheng,