Extramedullary hematopoiesis of the paranasal sinuses associated with moyamoya syndrome in sickle cell disease

Sickle cell disease is a common blood disorder with well-known clinical presentations including extramedullary hematopoiesis and moyamoya syndrome. However, it is extremely rare for extramedullary hematopoiesis to occur in the paranasal sinuses. Here, we present a case of a child with known homozygous sickle cell disease who has extramedullary hematopoiesis within the maxillary and the sphenoidal sinuses associated with moyamoya syndrome.