Atypical presentation of intracochlear schwannoma in a child

Intracochlear schwannoma (ICS) is a rare tumor that can cause significant hearing loss. Previous clinical reports on ICS have described this disease in adults. We present a pediatric patient with left-sided ICS who initially presented with a mild conductive hearing loss. We demonstrate the progression of the hearing loss over a span of several years through serial audiograms, as well as the process of diagnosis and treatment. This rare and unique case demonstrates that ICS can be found in young children.