Unusual neoplasms of the vulva

Unusual vulvar neoplasms comprise a small minority of general surgical pathology cases. We have limited our discussion to the following four vulvar tumours that were diagnosed at our institution during the past year: extramammary Paget disease; melanoma; granular cell tumour; and epithelioid sarcoma, proximal-type. We hope that the review will be of practical interest to the general surgical pathologist. Pathogenesis, clinical presentation, morphology, differential diagnosis, ancillary studies, prognosis, and treatment will be discussed.