| Article ID | Journal | Published Year | Pages | File Type |
|---|---|---|---|---|
| 4143946 | Anales de Pediatría | 2007 | 4 Pages |
Abstract
This entity should be considered in patients with acute metabolic acidosis and ketosis with normal glycemia and aciduria. The urine contains large amounts of 2-methylacetoacetate and its decarboxylation products. In the neonatal period, this inherited disorder of metabolism can produce severe hydroelectrolyte disorders in the form of a gradual process or acute episodes, which can occasionally be fatal.
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Authors
I. Cubillo Serna, J. Suárez Fernández, J.M. Merino Arribas, J. DÃaz Ruiz, C. Bustamante Hervás, C. De Frutos MartÃnez,