Currarino syndrome with intramedullary spinal cord abscess related communication between the tethered cord and a presacral mass: A case report

•We report the Currarino syndrome (CS) with crucial intramedullary spinal cord abscess.•Intramedullary spinal cord abscess is rare in CS and require immediate intervention.•We reviewed CS with crucial neurological infection, such as meningitis and abscess.•Surgical treatment of CS with neurological infectious condition remains uncertain.•We recommend to separate the connection to neural tube immediately.

We herein report the case of a 21-day-old boy in which the detection of an intramedullary spinal cord abscess led to the diagnosis of Currarino syndrome (CS). He had a complete phenotype of CS, including sacral agenesis, an anorectal malformation, a presacral mass, and spinal cord malformations. In addition, he had an intramedullary spinal cord abscess. Intramedullary spinal cord abscess is rare in CS and is thought to require immediate intervention. Therefore, we additionally reviewed the available literature and discussed the therapeutic approach for CS with an intramedullary cord abscess.