Gastric plexiform fibromyxoma tumor in a child – Case report and review of the literature

•Plexiform fibromyxoma is an exceedingly rare tumor in pediatric patients.•Symptoms and signs are non-specific, ranging from an incidental finding to gastric perforation.•The vast majority of these tumors are transmural tumors located in the distal stomach.•Diagnosis rests on immunohistochemistry staining showing evidence of myofibroblastic differentiation.

Plexiform fibromyxoma tumor (PFT) is an exceedingly rare tumor, particularly in children where only four cases have been reported to date. The patient reported herein presented with abdominal pain and vomiting related to gastric outlet obstruction caused by a large, polypoid PFT. We describe the clinical features, diagnostic evaluation, and surgical treatment of this rare tumor in our patient. Further, we review the literature of FPT to bring attention to this rare gastric tumor to the Pediatric Surgeon.