Long term survival in pediatric hepatic angiosarcoma (PHAS): A case report and review of the literature

•PHAS may be treated successfully with complete gross resection and chemotherapy.•Chemotherapy regimens for PHAS are not yet standardized.•Overall results for treatment of PHAS remain poor.

Pediatric hepatic angiosarcoma (PHAS) is extremely rare, with only five reported tumor-free survivors. Aggressive surgical resection and chemotherapy have been the management in all documented survivors of this disease, however no specific treatment guidelines are established. We present a case of PHAS with the longest reported tumor-free survival at over six years off therapy.