Angiomyolipoma of the tunica dartos of the scrotum in infancy

•Angiomyolipomas are benign mesenchymal tumors.•This is the first case of angiomyolipoma of the scrotum in infancy.•Although extremely rare, it should be considered in cases of scrotal tumor.

A 12-month-old boy presented with left scrotal swelling. The mass was irregular, soft, fleshy, and nontender. It adhered to the scrotal skin and gradually enlarged. Operative findings revealed a mass fixed to the scrotal fundus and diagnosed as angiomyolipoma. This is apparently the first report of scrotal angiomyolipoma in infancy.