Successful three stage repair of a large congenital abdominal region defect

We present two infants born with large, right upper quadrant defects which cannot be categorized as either a gastroschisis or omphalocele. We successfully managed one infant with a three stage repair using polytetrafluoroethylene (PTFE) patch, porcine urinary bladder matrix (UBM) and delayed surgical closure. The second infant passed away due to parental consent care withdrawal.