Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
4172229 | Paediatrics and Child Health | 2014 | 6 Pages |
Abstract
Juvenile dermatomyositis is the most common idiopathic inflammatory myopathy of childhood. Management focuses on early aggressive suppression of inflammation to induce sustained remission and prevent complications such as muscle contractures or calcinosis. Advances in diagnostic modalities and treatment have led to improved mortality and morbidity, but long-term risks remain significant. Early disease recognition with appropriate referral and management by a specialist multidisciplinary team is crucial. This review focuses on juvenile dermatomyositis including differential diagnosis from other conditions causing muscle weakness in children.
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Authors
Sunil Sampath, Liza J. McCann,