Autoimmune pancreatitis with multiple extrapancreatic manifestations

Autoimmune pancreatitis is a rare but increasingly recognised entity, which may account for up to 7% of cases of idiopathic chronic pancreatitis. There are several characteristic imaging features associated with the disease however it often mimics pancreatic malignancy both clinically and radiologically, and may result in unnecessary surgery being performed. While autoimmune pancreatitis may involve the pancreas in isolation, almost half of these patients have manifestations of the disease in other organs. These additional sites of involvement may be identifiable radiologically and, when present, help confirm the diagnosis. We present a case of autoimmune pancreatitis with multiple extrapancreatic manifestations and review the available literature.