Manifestaciones urológicas del síndrome de Peutz-Jeghers: presentación de 2 casos y revisión de la literatura

PJ patients have an increased risk of developing tumours in different organs, and although testicles are an uncommon site, its incidence is much higher than that of the general population, therefore monitoring should be performed in this group of patients with self-examination and regular visits, in order to actively look for signs that may indicate development of testicular disease. The most common histological type is the Sertoli cells tumour, which usually has a benign behaviour. So far, there are no histological, biological or imaging markers that predict their behaviour or metastatic potential. Their surgical management has changed according to the most recent literature reviewed, with partial orchiectomy and not radical orchiectomy being proposed as a viable option when the remaining testicular parenchyma is suitable for preservation.