| Article ID | Journal | Published Year | Pages | File Type |
|---|---|---|---|---|
| 4282366 | Annales de Chirurgie | 2006 | 5 Pages |
Abstract
Gastrointestinal involvement in Von Recklinghausen's neurofibromatosis (autosomal dominant disease) is observed in 25% of patients and is frequently represented by duodenal carcinoids. We report a case of somatostatinoma of the ampulla in a 42-year-old female with neurofibromatosis and pheochromocytoma and show a literature review about the association of neurofibromatosis and somatostatinoma. This pathological association appears non hasardous and surgical ampullectomy offers a good alternative to pancreaticoduodenectomy in localised tumors treatment.
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Authors
R. Caiazzo, C. Mariette, G. Piessen, T. Jany, B. Carnaille, J.-P. Triboulet,