Chordoid glioma: Case report and review of the literature

•We reported the 80th case of chordoid glioma and reviewed the literature.•Clinical outcomes reported have been poor.•If possible, efficient treatment depends upon radical surgical resection, however partial resection with adjuvant radiosurgery can be the most recommend due to local tumor and morbid-mortality relation.•No chemotherapeutic regimen has been shown to be effective for CG.

IntroductionChordoid glioma is a rare low-grade brain tumor originating from the anterior wall of the third ventricle.Case presentationA 13-year-old female with progressive intermittent holocranial headaches and a diagnosis of chordoid glioma underwent tumor resection in our neuro-oncology unit.DiscussionWe review all 79 cases of chordoid glioma reported in the literature so far, focusing on the diagnostic criteria, treatment options and prognosis.ConclusionEfficient treatment of chordoid glioma depends upon radical surgical resection. Based on the reviewed data, which showed high morbi-mortality rates for this kind of tumor, we recommend a more conservative treatment approach.