Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8265130 | Free Radical Biology and Medicine | 2018 | 7 Pages |
Keywords
E3-binding proteinalpha-ketoglutarate dehydrogenase complexASUE3BPKGDHCPDHcflavin adenine dinucleotideHDX-MSRMSDTRISGCs2-amino-2-hydroxymethyl-propane-1,3-diolNAD+/NADHROSEDTAEthylenediaminetetraacetic acidHumanFADX-ray crystallographyBis-trisOxidative stressPathogenic mutationProtein structureGlycine cleavage systemLADHLipoamide dehydrogenaseLipoic acidbranched-chain α-keto acid dehydrogenase complexroot mean square deviationwild typeasymmetric unitpyruvate dehydrogenase complexReactive oxygen species
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Authors
Eszter Szabo, Reka Mizsei, Piotr Wilk, Zsofia Zambo, Beata Torocsik, Manfred S. Weiss, Vera Adam-Vizi, Attila Ambrus,