Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8624392 | Oral Science International | 2018 | 7 Pages |
Abstract
Nevoid basal cell carcinoma syndrome (NBCCS) is an autosomal dominant disorder characterized by tumorigenesis and physical deformities. Although more than 50 clinical manifestations have been described, only two major criteria or one major and two minor criteria are necessary for diagnosis. The most frequently observed manifestation in the oral and the maxillofacial region is an odontogenic keratocyst. In this study, we describe a 14-year-old boy with a diagnosis of NBCCS who presented with a central odontogenic fibroma (COF) in the mandible. This report highlights the importance of precise diagnosis and the choice of surgical method for COF.
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Authors
Yasuyuki Shimada, Yohei Kawasaki, Michita Tayama, Junko Kindaichi, Yutaka Maruoka,