Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8653477 | Annals of Vascular Surgery | 2018 | 4 Pages |
Abstract
Abdominal aortic aneurysms (AAAs) are very rare in Marfan syndrome. We present a case with a young nonsmoking and normotensive male with Marfan syndrome, who developed an infrarenal AAA that presented with rupture to the retroperitoneal cavity causing life-threatening bleeding shock. The patient had acute aortic surgery and survived. Five months before this incident, the patient had uneventful elective aortic root replacement (ad modum David) due to an enlarged aortic root. At that time, his abdominal aorta was assessed with a routine ultrasound scan that showed a normal-sized abdominal aorta. This documents that the aneurysm had evolved very rapidly despite young age and absence of risk factors.
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Authors
Maria Weinkouff Pedersen, Khiem Dinh Huynh, Ulrik Thorngren Baandrup, Dorte Guldbrand Nielsen, Niels Holmark Andersen,