Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8713817 | Journal of Allergy and Clinical Immunology | 2018 | 54 Pages |
Abstract
RIC HCT resolves DNA repair disorder-associated immunodeficiency. Long-term follow-up is required for secondary malignancy surveillance. Routine HCT for AT is not recommended.
Keywords
DNA-DSBNHEJHCTGvHDATGSCIDAtaxia-telangiectasiaNBSLIG4PTLDcGVHDRICaGVHDanti-thymocyte globulinRAGnatural killerataxia-telangiectasia mutatedPosttransplantation lymphoproliferative disorderAcute graft-versus-host diseaseGraft-versus-host diseaseChronic graft-versus-host diseaseReduced-intensity conditioningMyeloablative conditioningATMNijmegen breakage syndromeDNA double-strand breakMACNonhomologous end-joiningHematopoietic cell transplantationHematopoietic stem cell transplantationRecombination-Activating Genesevere combined immunodeficiency
Related Topics
Life Sciences
Immunology and Microbiology
Immunology
Authors
James MD, Michael H. MD, Dmitry PhD, Bernd H. MD, Alice PhD, Jack PhD, Claire PhD, Jochen PhD, Rebecca H. MD, Marie MD, Elena MD, Katarzyna MD, Mary MD, Tobias MD, Andrea PhD, H. Bobby PhD, Sujal MD, Alfred MD, Andrew R. MD,