Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8811196 | Journal of Pediatric Surgery Case Reports | 2017 | 5 Pages |
Abstract
Neurenteric cysts (NECs), also called enterogenous cysts or enterogenic cysts, are congenital malformative anomalies of endodermal origin that manifest with a variety of disorders, including spine anomalies. Neurenteric cysts are uncommon developmental disorders reported in 0.7%-1.3% of all spinal tumors. Klippel-Feil syndrome (KFS) defines a malformative spine disorder presenting with congenital fusion of cervical vertebrae and/or other parts of the spine. In patients with KFS, NECs are rarely reported; they may be silent for long periods of time, showing a slow progressive course or manifesting with an acute, severe neurological presentation or with fluctuating myelopathic symptoms. We report a young patient affected by KFS associated with a NEC which, in a short period of time, progressively caused myelopathic symptomatology. Surgical intervention resulted in resolution of the neurological signs.
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Authors
Vito Pavone, Andrea D. Praticò, Rosario Caltabiano, Giuseppe Barbagallo, Raffaele Falsaperla, Piero Pavone, Saveria Spadola, Martino Ruggieri,