Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8811258 | Journal of Pediatric Surgery Case Reports | 2017 | 5 Pages |
Abstract
Ehlers-Danlos syndrome (EDS) is an inherited connective tissue disorder that is often associated with pectus excavatum (PE). The Nuss procedure, which is a minimally invasive approach for the treatment of PE achieves good functional and cosmetic outcomes. We experienced a case of EDS-associated asymmetric PE that was corrected by the Nuss procedure using chondrotomy of the costal cartilages. After this procedure, an excellent chest appearance was achieved. Our experience suggests that the repair of PE can be accomplished safely in EDS patients and that this procedure can achieve good cosmetic results in patients with asymmetric PE.
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Authors
Kazunori Masahata, Chizu Yoneyama, Ryo Tsukada, Chiyoshi Toyama, Souji Ibuka, Keigo Nara, Hideki Soh, Noriaki Usui,