Article ID Journal Published Year Pages File Type
8811258 Journal of Pediatric Surgery Case Reports 2017 5 Pages PDF
Abstract
Ehlers-Danlos syndrome (EDS) is an inherited connective tissue disorder that is often associated with pectus excavatum (PE). The Nuss procedure, which is a minimally invasive approach for the treatment of PE achieves good functional and cosmetic outcomes. We experienced a case of EDS-associated asymmetric PE that was corrected by the Nuss procedure using chondrotomy of the costal cartilages. After this procedure, an excellent chest appearance was achieved. Our experience suggests that the repair of PE can be accomplished safely in EDS patients and that this procedure can achieve good cosmetic results in patients with asymmetric PE.
Related Topics
Health Sciences Medicine and Dentistry Perinatology, Pediatrics and Child Health
Authors
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