Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8811277 | Journal of Pediatric Surgery Case Reports | 2017 | 4 Pages |
Abstract
We report the multi-modality treatment of a massive cervicothoracic lymphatic-venous malformation (LVM) in a 13-year-old boy that was present at birth as a small cervical mass. At four years of age, sclerotherapy significantly reduced the size of the malformation but over subsequent years the mass increased dramatically in size and resulted in a consumptive coagulopathy and limited left shoulder function. Treatment with sildenafil was without effect. The consumptive coagulopathy improved with subcutaneous enoxaparin. A multi-disciplinary team excised part of the mass when he was 11 years old. After surgery, gradual enlargement of the mass and rise in d-dimer prompted treatment with sirolimus. Two sessions of sclerotherapy arrested enlargement of the mass. Multi-modality treatment resulted in a marked reduction of the LVM in the child. However, enlargement of the mass and further treatment is anticipated as a cure has not yet been found.
Keywords
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Authors
Cynthia MD, FACS, FAAP, Taylor BS, Tania MD, Linda MD, Anna MD, Jimmy MD, Jason MD, Gresham MD,