Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8811409 | Journal of Pediatric Surgery Case Reports | 2016 | 4 Pages |
Abstract
Low-grade fibromyxoid sarcoma (LGFMS) is an extremely rare neoplasm classified as a fibroblastic soft tissue tumor. It has been described by its characteristic deceptively benign histological appearance with metastatic potential during long-term follow-up. We herein describe an 8-year-old boy with LGFMS located in the internal oblique muscle. Histological findings of the resected specimen included contrasting fibrous and myxoid areas with a swirling, whorled growth pattern; bland, benign-appearing fibroblastic spindle cells; and large collagen rosettes. Immunohistologic examination revealed mucin 4 positivity. The surgical margin of the tumor was obscure; therefore, we performed an additional resection 2 months later with a 1 cm margin from the edge of the tumor. No recurrence or metastasis was identified throughout 1 year of follow-up.
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Authors
Tatsuma Sakaguchi, Yoshinori Hamada, Yusuke Nakamura, Takeshi Shirai, Hiroshi Hamada, Masanori Kon,