Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8963303 | Neuromuscular Disorders | 2018 | 18 Pages |
Abstract
We present a case report of a 42 year old female, diagnosed at the age of 3 with Juvenile Dermatomyositis. The clinical course was severe and refractory to immunosuppressive therapy. Currently, she is mostly affected by severe muscle atrophy, large joint contractures, calcinosis, and a lipodystrophy associated metabolic syndrome with hypertriglyceridemia, insulin resistance, high total testosterone and hepatic steatosis. She developed Hodgkin´s lymphoma in the course of her disease. Personalized therapeutic choices are discussed as regards juvenile dermatomyositis complications.
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Authors
Inês Rego de Figueiredo, Sara Guerreiro Castro, Vera Bernardino, José Silva Nunes, Pedro Alves, Maria Francisca Moraes-Fontes,