History of a Patient with Sack-Barabas Syndrome (Ehlers Danlos Type IV)-16 Years of Recurrent Life-extending Open and Endovascular Surgery

The Sack-Barabas syndrome, the vascular type of Ehlers-Danlos syndrome type IV, is considered the most serious form of Ehlers-Danlos syndrome as the vascular system is prone to aneurysmatic degeneration and rupture without preference of anatomic regions. We report a patient with Sack-Barabas syndrome who was treated by one vascular surgeon for 16 years, from the first of many operations until death at the age of 27.