دانلود مقالات ISI درباره Mfn2 + ترجمه فارسی

PGC-1α overexpression via local transfection attenuates mitophagy pathway in muscle disuse atrophy

Keywords: PGC-1α; peroxisome proliferator-activated receptor gamma, coactivator 1 alpha; FoxO; forkhead box O; 4-HNE; 4-hydroxynonenal; Mul1; mitochondrial E3 ubiquitin protein ligase 1; PINK1; PTEN-induced putative kinase 1; Mfn2; mitofusin 2; mROS; mitochondrial

دانلود رایگان متن کامل مقاله ISI 31 صفحه سال انتشار : 2016 سفارش ترجمه

HDAC6 maintains mitochondrial connectivity under hypoxic stress by suppressing MARCH5/MITOL dependent MFN2 degradation

Keywords: Hypoxia; HDAC6; Mitochondrial connectivity; MARCH5; MFN2;

دانلود رایگان متن کامل مقاله ISI 23 صفحه سال انتشار : 2015 سفارش ترجمه

Organelle communication: Signaling crossroads between homeostasis and disease

Keywords: Organelles; Endoplasmic reticulum; Mitochondria; Calcium signaling; BNIP1; BCL2/adenovirus E1B interacting protein 1; Ca2+; calcium; CERT; ceramide transfer protein; CMT2A; Charcot-Marie-Tooth type 2A; Δψmt; mitochondrial transmembrane potential; Dr

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2014 سفارش ترجمه

Novel mitofusin 2 splice-site mutation causes Charcot-Marie-Tooth disease type 2 with prominent sensory dysfunction

Keywords: Charcot-Marie-Tooth; Hereditary motor and sensory neuropathy; MFN2; Mutation; Phenotype;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2014 سفارش ترجمه

Epigallocatechin gallate counteracts oxidative stress in docosahexaenoxic acid-treated myocytes

Keywords: AFU; arbitrary fluorescence units; Ant 1; adenine nucleotide translocase 1; Cox; cytochrome c oxidase subunit V; Cs; citrate synthase; DCFH-DA; 2′,7′-dichlorofluorescin diacetate; DHA; docosahexaenoic acid; DMEM; Dulbecco's modified Eagle's medium; Dr

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2014 سفارش ترجمه

Metabolic and transcriptional responses of gilthead sea bream (Sparus aurata L.) to environmental stress: New insights in fish mitochondrial phenotyping

Keywords: ACAA2; 3-ketoacyl-CoA thiolase, mitochondrial; AIFM1; apoptosis-related protein 1; AIFM3; apoptosis-related protein 3; ANOVA; analysis of variance; BAX; apoptosis regulator BAX; BCL2; apoptosis regulator Bcl-2; BCLX; Bcl-2-like protein 1; CAT; catalase; C

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2014 سفارش ترجمه

Inhibition of ERK-DLP1 signaling and mitochondrial division alleviates mitochondrial dysfunction in Alzheimer's disease cybrid cell

Keywords: AD; Alzheimer's disease; mtDNA; Mitochondrial DNA; DLP1; Dynamin-like protein; Mfn2; Mitofusin 2; ERK; Extracellular signal-regulated kinase; Aβ; Amyloid beta peptide; CcO; Cytochrome c oxidase; ROS; Reactive oxygen species; PD; Parkinson disease; HD; Hu

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2014 سفارش ترجمه

Mitochondrial dysfunction as a central actor in intellectual disability-related diseases: An overview of Down syndrome, autism, Fragile X and Rett syndrome

Keywords: Intellectual disability; Mitochondria; Mitochondrial dysfunction; Oxidative phosphorylation; Neurogenesis; Neuroplasticity; Down syndrome; Rett syndrome; Autism; Fragile X; Oxidative stress; Drug development; Epigallocatechine-3-gallate; ANT; adenine nucl

دانلود رایگان متن کامل مقاله ISI 16 صفحه سال انتشار : 2014 سفارش ترجمه

Accelerated recovery of renal mitochondrial and tubule homeostasis with SIRT1/PGC-1α activation following ischemia-reperfusion injury

Keywords: SIRT1; sirtuin 1; PGC-1α; peroxisome proliferator activated receptor γ coactivator-1α; ATPβ; ATP synthase subunit β; COX I; cytochrome c oxidase subunit I; NDUFB8; NADH dehydrogenase (ubiquinone) 1 beta subcomplex 8; Drp1; dynamin related protein 1;

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2013 سفارش ترجمه

Copper deficiency alters cell bioenergetics and induces mitochondrial fusion through up-regulation of MFN2 and OPA1 in erythropoietic cells

Keywords: Mitochondria; Bioenergetics; Copper; Glycolysis; MFN2; OPA1; Mitochondrial dynamics;

دانلود رایگان متن کامل مقاله ISI 23 صفحه سال انتشار : 2013 سفارش ترجمه

Endoplasmic reticulum: ER stress regulates mitochondrial bioenergetics

Keywords: ASK1; apoptosis signal-regulating kinase 1; ATF4; activating transcription factor 4; ATF6; activating transcription factor 6; BAX; Bcl2 associated X protein; BAK; BCL2-antagonist/killer; CHOP; C/EBP-homologous protein; eIF2α; eukaryotic initiation factor

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2012 سفارش ترجمه

Mitofusin 1 inhibits an apoptosis-associated amino-terminal conformational change in Bax, but not its mitochondrial translocation, in a GTPase-dependent manner

Keywords: Apoptosis; Bax; Mitochondria; Mitofusin; Mfn1; Mfn2; Outer mitochondrial membrane

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2012 سفارش ترجمه

Standardized mitochondrial analysis gives new insights into mitochondrial dynamics and OPA1 function

Keywords: OPA1, optic atrophy 1; MFN2, mitofusin 2; GDAP1, ganglioside-induced differentiation-associated-protein 1; CCCP, carbonyl cyanide 3-chlorophenylhydrazone; MTOC, microtubule organizing centreMitochondrial dynamics; OPA1; MFN2; Microtubule organizing centre

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2012 سفارش ترجمه

Mitochondrial chaperone DnaJA3 induces Drp1-dependent mitochondrial fragmentation

Keywords: Aco1; aconitase; antA; antimycin A; CCCP; carbonyl cyanide m-chlorophenyl hyzdrazin; COXIV; cyclooxygenase IV; DsRed2; Discosoma sp. Red Fluorescent Protein; Drp1; dynamin-related protein 1; EGFP; Enhanced Green Fluorescent Protein; HBSS; Hank's Buffered

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2012 سفارش ترجمه

Characterizing the phenotypic manifestations of MFN2 R104W mutation in Charcot-Marie-Tooth type 2

Keywords: Charcot-Marie-Tooth disease; CMT2A; Hereditary motor and sensory neuropathy; MFN2; R104W mutation;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2011 سفارش ترجمه

Mitogen-activated protein kinase kinases promote mitochondrial biogenesis in part through inducing peroxisome proliferator-activated receptor γ coactivator-1β expression

Keywords: ATP5b; ATP synthase; cyt-C; cytochrome-C; ERRα and ERRγ; estrogen-related receptors α and γ; ERK1/2; extracellular signal-regulated kinases; Tfam; mitochondrial transcription factor A; Mfn2; mitofusin 2; MEK1/2; mitogen-activated protein kinase kinase

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2011 سفارش ترجمه

Protective effects of resveratrol through the up-regulation of SIRT1 expression in the mutant hSOD1-G93A-bearing motor neuron-like cell culture model of amyotrophic lateral sclerosis

Keywords: ALS; amyotrophic lateral sclerosis; VSC 4.1; ventral spinal cord 4.1 cells; hSOD1; human superoxide dismutase 1; wt; wild type; SIRT1; silent mating type information regulation 2 homolog 1; DMEM; Dulbecco's modified Eagle's medium; FBS; fetal bovine serum

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2011 سفارش ترجمه

Developmental defects and neuromuscular alterations due to mitofusin 2 gene (MFN2) silencing in zebrafish: a new model for Charcot-Marie-Tooth type 2A neuropathy

Keywords: Peripheral neuropathy; CMT2A; MFN2; Zebrafish; Axonal degeneration

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2011 سفارش ترجمه

Mitochondrial dysfunction and Alzheimer's disease

Keywords: ABAD; amyloid-beta (Aβ) binding alcohol dehydrogenase; AD; Alzheimer's disease; APOE2; Apolipoprotein E epsilon-2 allele; APOE3; Apolipoprotein E epsilon-3 allele; APOE4; Apolipoprotein E epsilon-4 allele; APP; amyloid precursor protein; ATP; Adenosine-5

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2011 سفارش ترجمه

Mitofusin-2 is a novel direct target of p53

Keywords: Mfn2; P53; Promoter; Transcription; Chromatin immunoprecipitation;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2010 سفارش ترجمه

Mitofusin-2 protects against cold stress-induced cell injury in HEK293 cells

Keywords: Mitochondria; Mfn2; Cold stress; Drp1; ATP

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2010 سفارش ترجمه

Role of mitofusin 2 mutations in the physiopathology of Charcot–Marie–Tooth disease type 2A

Keywords: Charcot–Marie–Tooth disease; Neuropathy; Mfn2; Mitochondrial fusion

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2009 سفارش ترجمه

Two Spanish families with Charcot-Marie-Tooth type 2A: Clinical, electrophysiological and molecular findings

Keywords: MFN2; CMT 2; Axonal Charcot; CMT 2A; Mitofusin 2; CMT; Charcot-Marie-Tooth;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2008 سفارش ترجمه

Mitochondrial fusion and function in Charcot–Marie–Tooth type 2A patient fibroblasts with mitofusin 2 mutations

Keywords: CMT2A; Peripheral neuropathy; Mitochondria; Mitofusin; Mfn2; Mfn1; GTPase; Membrane fusion; Fibroblasts

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2008 سفارش ترجمه