Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
10833009 | Molecular Genetics and Metabolism | 2013 | 7 Pages |
Abstract
The data presented here strongly support glutathione as a “redox blood signature” in mitochondrial disorders and its use as a clinical trial endpoint in the development of mitochondrial disease therapies.
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Authors
Anna Pastore, Sara Petrillo, Giulia Tozzi, Rosalba Carrozzo, Diego Martinelli, Carlo Dionisi-Vici, Gianna Di Giovamberardino, Ferdinando Ceravolo, Matthew B. Klein, Guy Miller, Gregory M. Enns, Enrico Bertini, Fiorella Piemonte,