| Article ID | Journal | Published Year | Pages | File Type |
|---|---|---|---|---|
| 10833100 | Molecular Genetics and Metabolism | 2013 | 7 Pages |
Abstract
⺠Metabolism during exercise and exercise tolerance were examined in the patients. ⺠The peak oxidative capacity was abnormally low. ⺠Exercise intolerance with excessive fatigue was evident in the patients. ⺠However, a glucose infusion significantly improved exercise capacity. ⺠GSD type IIIa thus includes dynamic exercise-related symptoms of muscle fatigue. ⺠This is due to insufficient energy production in skeletal muscle during exercise.
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Authors
Nicolai Preisler, Agnès Pradel, Edith Husu, Karen Lindhardt Madsen, Marie-Hélène Becquemin, Alix Mollet, Philippe Labrune, Francois Petit, Jean-Yves Hogrel, Claude Jardel, Francois Maillot, John Vissing, Pascal Laforêt,