| Article ID | Journal | Published Year | Pages | File Type |
|---|---|---|---|---|
| 11010909 | Molecular Genetics and Metabolism | 2018 | 6 Pages |
Abstract
Chronic treatment with pirfenidone may provide clinical benefit with few adverse effects for some patients with HPS pulmonary fibrosis. These results suggest that compassionate use of pirfenidone could be considered on a case-by-case basis for patients with HPS pulmonary fibrosis.
Related Topics
Life Sciences
Biochemistry, Genetics and Molecular Biology
Biochemistry
Authors
Kevin J. O'Brien, Wendy J. Introne, Orhan Akal, Tulay Akal, Adrian Barbu, Melissa P. McGowan, Melissa A. Merideth, Samuel L. Jr, William A. Gahl, Bernadette R. Gochuico,