Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
2678565 | Pediatria Polska | 2016 | 5 Pages |
Abstract
Caroli's disease is a rare congenital disease of the liver characterized by multiple segmental cystic dilatation of intrahepatic bile ducts. The disease is referred as Caroli's syndrome when it is associated with congenital hepatic fibrosis. The clinical features include jaundice, right upper abdominal pain, and fever due to the associated complications of bacterial cholangitis. Owing to the rarity of this disorder, the diagnosis and treatment is often delayed.
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Authors
Patryk LipiÅski, Dorota Wicher, Piotr KaliciÅski, Joanna Cielecka-Kuszyk, Irena Jankowska,