Impacted tooth extraction from osteoma in a patient with Robinow syndrome diagnosed from intraoral lesions: A case report and literature review

Robinow syndrome is very rare and is characterized by congenital anomalies of the head and neck. Symptoms occurring in the head and neck region include osteosclerosis of the skull, midface hypoplasia, cleft palate, and impacted teeth. There is no case report describing oral maxillofacial surgery in Robinow syndrome. We report the case of a 19-year-old female in whom a panoramic radiograph revealed a radiopaque lesion in the right maxillary molar region along with multiple impacted teeth, hypodontia, and retained deciduous teeth in her jaws. Impacted tooth was also present in the radiopaque lesion on the right maxilla. Computed tomography revealed a high-density area on the right maxilla, representing a lesion containing an impacted tooth. The general findings and the presence of impacted teeth indicated symptomatic disease, and biopsy examination confirmed an osteoma. After additional examinations, Robinow syndrome was diagnosed. Tooth extraction was performed under general anesthesia. About 8 months after operation, the wound showed epithelialization and osteoma-like tissue formation was confirmed in the extraction socket. We considered repeated observations to be necessary in this case because of the possibility of recurrence. It is necessary to be aware of the possible diagnosis of Robinow syndrome on the basis of intraoral symptoms after school age.