Hipertensión pulmonar en cardiopatías congénitas del adulto

Pulmonary arterial hypertension is commonly found in adults with congenital heart diseases. The magnitude of the compromise will depend on the type of defect, the time of the correction, and the haemodynamic repercussion, and, in turn will be an essential determining factor in the possibility of performing corrective management in those patients with delayed diagnoses. A review is presented on the information available as regards the classification, diagnosis, and management depending on the possibility of intervention, the general treatment, and use of pulmonary vasodilators, with an emphasis on the special recommendations for the management of patients with Eisenmenger syndrome.