Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
8323565 | The International Journal of Biochemistry & Cell Biology | 2014 | 9 Pages |
Abstract
This article is part of a Directed Issue entitled: Cystic Fibrosis: From o-mics to cell biology, physiology, and therapeutic advances.
Keywords
NBDICMrAAVforskolinIPSCCFTRNMDABPsMSDFskPDEPTCsRho-kinaseEMATMAOrganoidsTrimethylangelicinPRSNHERFFISHTSFDANa+/H+ exchanger regulatory factorpharmacological chaperonesEuropean Medicines agencyFood & Drug AdministrationAlinucleotide binding domainmembrane spanning domainair–liquid interfacePCscystic fibrosis transmembrane conductance regulatorInduced pluripotent stem cellshigh-throughput screeningnonsense-mediated mRNA decayPhosphodiesteraseCystic fibrosiswild-typerecombinant adeno-associated virusPersonalized medicinecalCRCpremature termination codonsRock
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Authors
Pauline T. Ikpa, Marcel J.C. Bijvelds, Hugo R. de Jonge,