Article ID Journal Published Year Pages File Type
8924074 IHJ Cardiovascular Case Reports (CVCR) 2018 6 Pages PDF
Abstract
Rosai-Dorfman disease (RDD) is a non-malignant disease. Pathologically it is characterised by histiocytic proliferation. A typical clinical presentation is painless generalised lymphadenopathy. Extra nodal involvement can be seen in 20-40% of cases. Cardiac involvement is rare and suggests a poor prognosis. We report a case of RDD with extensive cardiac involvement, initially masquerading as multiple cardiac thrombi in the background of underlying antiphospholipid antibody syndrome.
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